{"id":52218,"date":"2018-02-07T13:00:33","date_gmt":"2018-02-07T10:00:33","guid":{"rendered":"https:\/\/sanatate.md\/?page_id=52218"},"modified":"2018-02-07T13:04:30","modified_gmt":"2018-02-07T10:04:30","slug":"acrodermatita-enteropatica","status":"publish","type":"page","link":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/","title":{"rendered":"Acrodermatita enteropatic\u0103"},"content":{"rendered":"<p>Acrodermatita enteropatic\u0103 este o anomalie ereditar\u0103, autozomal recesiv\u0103, caracterizat\u0103 prin dereglarea metabolic\u0103 a absorb\u0163iei zincului \u015fi manifestat\u0103 prin diaree, dermatit\u0103 \u015fi alopecie.<\/p>\n<p>Au existat cazuri, c\u00e2nd boala avea caracter dob\u00e2ndit, datorit\u0103 faptului, c\u0103 organismul nu primea cantitatea potrivit\u0103 de zinc.\u00a0\u00cen aceste cazuri, copiii au fost trecu\u0163i la hran\u0103 artificial\u0103 pentru a compensa deficitul.<\/p>\n<p>Maladia apare cel mai frecvent la copiii cu v\u00e2rsta cuprins\u0103 \u00eentre 4 s\u0103pt\u0103m\u00e2ni \u0219i 2 ani. \u00cen cazuri rare un astfel de diagnostic se depisteaz\u0103 la adolescen\u021bi \u0219i adul\u021bi.\u00a0Trebuie remarcat faptul, c\u0103 acrodermatita enteropatic\u0103 este o boal\u0103 rar\u0103 \u0219i adesea e confundat\u0103 cu boli cum ar fi dermatita, candidoza, epidermoliza buboas\u0103.<\/p>\n<h3>Motivele<\/h3>\n<p>Cauza principal\u0103 a acestei boli este \u00eenc\u0103lcarea absorb\u021biei de zinc \u00een intestin.<br \/>\nCopiii nou-n\u0103scu\u021bi au propriul lor factor, care leag\u0103 zincul \u0219i contribuie la absorb\u021bia acestuia. Procesul dat se nume\u0219te ligand de legare a zincului, dar datorit\u0103 unui defect genetic, intr\u00e2nd \u00een organismul copilului cu laptele matern, el nu este activ.<\/p>\n<p>Exist\u0103, de asemenea, o teorie privind \u00eenc\u0103lcarea capacit\u0103\u021bii de lucru a intestinului sub\u021bire \u0219i o sc\u0103dere a sintezei enzimelor sale.\u00a0\u00cen consecin\u0163\u0103 zincul nu este absorbit, iar datorit\u0103 defec\u021biunii men\u021bionate mai sus, exist\u0103 probleme cu asimilarea acestuia de c\u0103tre organismul copilului.<\/p>\n<p>Cauza bolii sunt c\u0103s\u0103toriile de s\u00e2nge, care duc la caracterul genetic al bolii, observat\u0103 \u00een 20-30% din toate cazurile.<\/p>\n<p>Dac\u0103 boala e dob\u00e2ndit\u0103 &#8211; este frecvent\u0103 \u00een \u00eentreaga familie.<\/p>\n<h3>Simptomele<\/h3>\n<p>Zincul are un rol important \u00een organismul uman.\u00a0Particip\u0103 la metabolizarea lipidelor \u0219i proteinelor, formarea sistemului imunitar, reduce riscul apari\u021biei bolilor cardiovasculare.<\/p>\n<p>Simptomele comune ale deficien\u021bei de zinc:<\/p>\n<ul>\n<li>exacerb\u0103rile frecvente \u0219i dificile ale bolilor cronice existente;<\/li>\n<li>infec\u021bii virale;<\/li>\n<li>iritabilitatea constant\u0103 \u015fi inexplicabil\u0103, somnolen\u021ba, indiferen\u0163a.<\/li>\n<\/ul>\n<p>Simptomele caracteristice:<\/p>\n<ul>\n<li>Erup\u0163ii pe piele: ele sunt simetrice, situate \u00een pliurile naturale ale corpului, \u00een zona labei m\u00e2inilor \u0219i t\u0103lpilor picioarelor, \u00een jurul deschiderilor naturale (gur\u0103, ochi, canal anal, vagin). Specific erup\u021biei cutanate este caracterul polimorf reprezentat de bule.\u00a0Acestea sunt umede \u015fi erodate, au cruste purulente sau seroase-purulente.\u00a0De regul\u0103, apar la copii.<\/li>\n<li>Procese inflamatorii ale cavit\u0103\u021bii bucale: inflama\u021bia limbii, stomatita, fisuri la nivelul buzelor \u0219i col\u021burilor gurii.<\/li>\n<li>Respingerea pl\u0103cilor de unghii.<\/li>\n<li>Alopecia, adesea total\u0103.<\/li>\n<li>Probleme cu ochii &#8211; conjunctivit\u0103, blefarit\u0103.\u00a0Exist\u0103 o fotofobie manifestat\u0103 brusc.<\/li>\n<li>Probleme cu tractul gastrointestinal &#8211; tulbur\u0103ri de dispepsie (diaree care apare de 20 &#8211; 30 de ori pe zi).<\/li>\n<\/ul>\n<h3>Diagnosticare<\/h3>\n<p>La \u00eenceput se colecteaz\u0103 o anamnez\u0103 (dac\u0103 pacientul\u00a0 e copil &#8211; se discut\u0103 cu p\u0103rin\u021bii acestuia):\u00a0 dac\u0103 exist\u0103 \u00een familie boli genetice, au fost factori de risc care ar fi putut provoca dezvoltarea bolii.<\/p>\n<p>Apoi se face o examinare general\u0103 a pacientului: se atrage aten\u021bia asupra erup\u021biei cutanate existente, problemelor \u00een cavitatea bucal\u0103 (amigdalite, stomatit\u0103, glosit\u0103), st\u0103rii unghiilor \u0219i p\u0103rului,\u00a0 diareei.\u00a0\u00cen plus, c\u00e2nd este examinat, medicul verific\u0103 reflexele, ceea ce demonstreaz\u0103 dac\u0103 exist\u0103 probleme cu sistemul nervos central.<\/p>\n<p>De asemenea, se efectueaz\u0103 un examen la ginecolog, proctolog, cardiolog (pentru probleme cu sistemul cardiovascular), gastroenterolog.<\/p>\n<p>Metodele de diagnostic de laborator pot ajuta la identificarea deficitului de zinc \u00een organism \u0219i a unui ligand de legare a zincului.\u00a0Un test de s\u00e2nge va ar\u0103ta o cre\u0219tere a ratei de sedimentare a eritrocitelor, leucocitelor, sc\u0103derea nivelului total de proteine, calciu \u0219i fosfor.<\/p>\n<p>Se efectueaz\u0103 diagnosticarea diferen\u021biat\u0103 cu astfel de boli cum ar fi epidermoliza buboas\u0103, candidoza sistemic\u0103, impetigo.<\/p>\n<p>Diagnosticul se face dup\u0103 eliminarea bolilor men\u021bionate mai sus \u0219i prezen\u0163a erup\u021biilor cutanate caracteristice pe piele.<\/p>\n<h3>Tratamentul<\/h3>\n<p>Tratamentul acestei boli const\u0103 \u00een restabilirea unui nivel sc\u0103zut de zinc \u00een organism.\u00a0 Sugarii, incapabili s\u0103 m\u0103n\u00e2nce independent, sunt trecu\u0163i la alimenta\u021bia artificial\u0103 cu preparate de zinc.\u00a0Copii mai mari \u0219i adul\u021bii completeaz\u0103 deficitul pe cale oral\u0103, adic\u0103\u00a0 iau preparate de zinc \u00eempreun\u0103 cu alimentele.\u00a0Tratamentul d\u0103 rezultate dup\u0103 10 zile: erup\u021biile cutanate \u00eencep s\u0103 dispar\u0103, p\u0103rul nu mai cade \u0219i unghiile revin la normal. Copilul \u00eencepe s\u0103 adauge \u00een greutate.<\/p>\n<p>\u00cen plus se prescriu\u00a0 antibacteriene \u0219i antiprotozoale.<\/p>\n<p>Simptomatic se prescriu vitaminele A, C, medicamente pentru tratamentul candidozei, albumine, globuline.<\/p>\n<p>Dac\u0103 boala este sever\u0103, sunt prescrise &#8211; hidrocortizon, dexametazon, prednizolon.<\/p>\n<p>Preparatele enzime sunt recomandate pentru a normaliza microflora intestinal\u0103 \u0219i o diet\u0103 \u00eembog\u0103\u021bit\u0103 cu zinc (carne de porc, ficat, pe\u0219te, carne de vit\u0103, file de pui).<\/p>\n<p>Pentru tratamentul extern al erup\u021biilor se aplic\u0103 solu\u021bie de verde de briliant, Fukortsin, past\u0103 de zinc, solu\u0163ii speciale cu zinc.<\/p>\n<p>Eficacitatea tratamentului depinde de alegerea corect\u0103 a medicamentelor, de diagnosticare \u0219i tratamentul la timp.\u00a0\u00cen caz contrar, poate surveni un rezultat letal, din cauza epuiz\u0103rii organismului \u0219i infec\u021biilor secundare.<\/p>\n<p>Dup\u0103 tratament, pacientul este luat la eviden\u0163\u0103.\u00a0De asemenea, el poate lua preparate de zinc pe via\u021b\u0103.\u00a0Depinde de gravitatea bolii \u0219i de caracteristicile individuale ale organismului.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Acrodermatita enteropatic\u0103 este o anomalie ereditar\u0103, autozomal recesiv\u0103, caracterizat\u0103 prin dereglarea metabolic\u0103 a absorb\u0163iei zincului \u015fi manifestat\u0103 prin diaree, dermatit\u0103 \u015fi alopecie. Au existat cazuri, c\u00e2nd boala avea caracter dob\u00e2ndit, datorit\u0103 faptului, c\u0103 organismul nu primea cantitatea potrivit\u0103 de zinc.\u00a0\u00cen aceste cazuri, copiii au fost trecu\u0163i la hran\u0103 artificial\u0103 pentru a compensa deficitul. Maladia apare [&hellip;]<\/p>\n","protected":false},"author":28,"featured_media":0,"parent":43635,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false,"footnotes":""},"class_list":["post-52218","page","type-page","status-publish"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Acrodermatita enteropatic\u0103 | Sanatate.md<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/\" \/>\n<meta property=\"og:locale\" content=\"ro_RO\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Acrodermatita enteropatic\u0103 | Sanatate.md\" \/>\n<meta property=\"og:description\" content=\"Acrodermatita enteropatic\u0103 este o anomalie ereditar\u0103, autozomal recesiv\u0103, caracterizat\u0103 prin dereglarea metabolic\u0103 a absorb\u0163iei zincului \u015fi manifestat\u0103 prin diaree, dermatit\u0103 \u015fi alopecie. Au existat cazuri, c\u00e2nd boala avea caracter dob\u00e2ndit, datorit\u0103 faptului, c\u0103 organismul nu primea cantitatea potrivit\u0103 de zinc.\u00a0\u00cen aceste cazuri, copiii au fost trecu\u0163i la hran\u0103 artificial\u0103 pentru a compensa deficitul. Maladia apare [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/\" \/>\n<meta property=\"og:site_name\" content=\"Sanatate.md\" \/>\n<meta property=\"article:modified_time\" content=\"2018-02-07T10:04:30+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Timp estimat pentru citire\" \/>\n\t<meta name=\"twitter:data1\" content=\"4 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/boli-si-tratament\\\/bolile-copiilor\\\/acrodermatita-enteropatica\\\/\",\"url\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/boli-si-tratament\\\/bolile-copiilor\\\/acrodermatita-enteropatica\\\/\",\"name\":\"Acrodermatita enteropatic\u0103 | Sanatate.md\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/#website\"},\"datePublished\":\"2018-02-07T10:00:33+00:00\",\"dateModified\":\"2018-02-07T10:04:30+00:00\",\"breadcrumb\":{\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/boli-si-tratament\\\/bolile-copiilor\\\/acrodermatita-enteropatica\\\/#breadcrumb\"},\"inLanguage\":\"ro-RO\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\\\/\\\/sanatate.md\\\/ro\\\/boli-si-tratament\\\/bolile-copiilor\\\/acrodermatita-enteropatica\\\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/boli-si-tratament\\\/bolile-copiilor\\\/acrodermatita-enteropatica\\\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"\u0413\u043b\u0430\u0432\u043d\u0430\u044f \u0441\u0442\u0440\u0430\u043d\u0438\u0446\u0430\",\"item\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Boli si tratament\",\"item\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/boli-si-tratament\\\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Bolile copiilor\",\"item\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/boli-si-tratament\\\/bolile-copiilor\\\/\"},{\"@type\":\"ListItem\",\"position\":4,\"name\":\"Acrodermatita enteropatic\u0103\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/#website\",\"url\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/\",\"name\":\"Sanatate.md\",\"description\":\"\u0416\u0443\u0440\u043d\u0430\u043b \u0434\u043b\u044f \u0432\u0441\u0435\u0439 \u0441\u0435\u043c\u044c\u0438 \u0432 \u041c\u043e\u043b\u0434\u043e\u0432\u0435\",\"publisher\":{\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/#organization\"},\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"ro-RO\"},{\"@type\":\"Organization\",\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/#organization\",\"name\":\"SANATATE\",\"url\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/\",\"logo\":{\"@type\":\"ImageObject\",\"inLanguage\":\"ro-RO\",\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/#\\\/schema\\\/logo\\\/image\\\/\",\"url\":\"https:\\\/\\\/sanatate.md\\\/wp-content\\\/uploads\\\/2022\\\/01\\\/sanatate-logo.svg\",\"contentUrl\":\"https:\\\/\\\/sanatate.md\\\/wp-content\\\/uploads\\\/2022\\\/01\\\/sanatate-logo.svg\",\"width\":\"1024\",\"height\":\"1024\",\"caption\":\"SANATATE\"},\"image\":{\"@id\":\"https:\\\/\\\/sanatate.md\\\/ro\\\/#\\\/schema\\\/logo\\\/image\\\/\"}}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Acrodermatita enteropatic\u0103 | Sanatate.md","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/","og_locale":"ro_RO","og_type":"article","og_title":"Acrodermatita enteropatic\u0103 | Sanatate.md","og_description":"Acrodermatita enteropatic\u0103 este o anomalie ereditar\u0103, autozomal recesiv\u0103, caracterizat\u0103 prin dereglarea metabolic\u0103 a absorb\u0163iei zincului \u015fi manifestat\u0103 prin diaree, dermatit\u0103 \u015fi alopecie. Au existat cazuri, c\u00e2nd boala avea caracter dob\u00e2ndit, datorit\u0103 faptului, c\u0103 organismul nu primea cantitatea potrivit\u0103 de zinc.\u00a0\u00cen aceste cazuri, copiii au fost trecu\u0163i la hran\u0103 artificial\u0103 pentru a compensa deficitul. Maladia apare [&hellip;]","og_url":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/","og_site_name":"Sanatate.md","article_modified_time":"2018-02-07T10:04:30+00:00","twitter_card":"summary_large_image","twitter_misc":{"Timp estimat pentru citire":"4 minute"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"WebPage","@id":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/","url":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/","name":"Acrodermatita enteropatic\u0103 | Sanatate.md","isPartOf":{"@id":"https:\/\/sanatate.md\/ro\/#website"},"datePublished":"2018-02-07T10:00:33+00:00","dateModified":"2018-02-07T10:04:30+00:00","breadcrumb":{"@id":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/#breadcrumb"},"inLanguage":"ro-RO","potentialAction":[{"@type":"ReadAction","target":["https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/"]}]},{"@type":"BreadcrumbList","@id":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/acrodermatita-enteropatica\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"\u0413\u043b\u0430\u0432\u043d\u0430\u044f \u0441\u0442\u0440\u0430\u043d\u0438\u0446\u0430","item":"https:\/\/sanatate.md\/ro\/"},{"@type":"ListItem","position":2,"name":"Boli si tratament","item":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/"},{"@type":"ListItem","position":3,"name":"Bolile copiilor","item":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/bolile-copiilor\/"},{"@type":"ListItem","position":4,"name":"Acrodermatita enteropatic\u0103"}]},{"@type":"WebSite","@id":"https:\/\/sanatate.md\/ro\/#website","url":"https:\/\/sanatate.md\/ro\/","name":"Sanatate.md","description":"\u0416\u0443\u0440\u043d\u0430\u043b \u0434\u043b\u044f \u0432\u0441\u0435\u0439 \u0441\u0435\u043c\u044c\u0438 \u0432 \u041c\u043e\u043b\u0434\u043e\u0432\u0435","publisher":{"@id":"https:\/\/sanatate.md\/ro\/#organization"},"potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/sanatate.md\/ro\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"ro-RO"},{"@type":"Organization","@id":"https:\/\/sanatate.md\/ro\/#organization","name":"SANATATE","url":"https:\/\/sanatate.md\/ro\/","logo":{"@type":"ImageObject","inLanguage":"ro-RO","@id":"https:\/\/sanatate.md\/ro\/#\/schema\/logo\/image\/","url":"https:\/\/sanatate.md\/wp-content\/uploads\/2022\/01\/sanatate-logo.svg","contentUrl":"https:\/\/sanatate.md\/wp-content\/uploads\/2022\/01\/sanatate-logo.svg","width":"1024","height":"1024","caption":"SANATATE"},"image":{"@id":"https:\/\/sanatate.md\/ro\/#\/schema\/logo\/image\/"}}]}},"_links":{"self":[{"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/pages\/52218","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/users\/28"}],"replies":[{"embeddable":true,"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/comments?post=52218"}],"version-history":[{"count":0,"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/pages\/52218\/revisions"}],"up":[{"embeddable":true,"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/pages\/43635"}],"wp:attachment":[{"href":"https:\/\/sanatate.md\/ro\/wp-json\/wp\/v2\/media?parent=52218"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}