{"id":54283,"date":"2018-03-13T12:38:28","date_gmt":"2018-03-13T09:38:28","guid":{"rendered":"https:\/\/sanatate.md\/?page_id=54283"},"modified":"2018-03-13T12:38:28","modified_gmt":"2018-03-13T09:38:28","slug":"amiotrofia-spinala-la-copii-werdnig-hoffmann","status":"publish","type":"page","link":"https:\/\/sanatate.md\/ro\/boli-si-tratament\/boli-ale-sistemului-musculo-scheletic-traumatisme\/amiotrofia-spinala-la-copii-werdnig-hoffmann\/","title":{"rendered":"Amiotrofia spinal\u0103 la copii \u2013 Werdnig-Hoffmann"},"content":{"rendered":"<p>Principala caracteristic\u0103 este sl\u0103biciunea muscular\u0103 asociat\u0103 de atrofia mu\u015fchilor. Boala se dezvolt\u0103 \u00een copil\u0103ria timpurie.<\/p>\n<p>E cauzat\u0103 de astfel de factori:<\/p>\n<ul>\n<li>a modific\u0103rilor \u00een celulele cornului anterior spinal, prin procesul degenerativ cu o progresie clar\u0103;<\/li>\n<li>a schimb\u0103rilor de origine secundar\u0103 \u00een celulele nervoase, precum \u0219i \u00een \u021besutul muscular.<\/li>\n<\/ul>\n<h3>\u00a0Cauzele<\/h3>\n<p>Amiotrofia spinal\u0103 Werding-Hoffmann este ereditar\u0103.\u00a0Conform cercet\u0103rilor, aceast\u0103 boal\u0103 are un procent ridicat de rudenie de s\u00e2nge al p\u0103rin\u0163ilor bolnavului.<\/p>\n<h3>Simptomatologia<\/h3>\n<p>Simptomele tipice ale bolii sunt sl\u0103biciunea \u0219i atrofia muscular\u0103, \u00een principal \u00een trunchi \u0219i extremit\u0103\u021bi.<\/p>\n<h3>Diagnosticarea<\/h3>\n<p>Tipul congenital este determinat \u00een maternitate, deoarece se observ\u0103 o hipotonie muscular\u0103 pronun\u021bat\u0103, precum \u0219i pozi\u021bia corpului copilului (membrele inferioare sunt desf\u0103\u0219urate \u00een afar\u0103, au o pozi\u021bie plat\u0103 pe suprafa\u021b\u0103, membrele superioare sunt orientate de-a lungul trunchiului, iar umerii sunt u\u015for ridica\u0163i).<br \/>\nLa copil se observ\u0103 o activitate a sistemului motoric involuntar\u0103, dar poate doar ocazional foarte rar mi\u015fc\u0103 degetele.<\/p>\n<h3>Tratamentul<\/h3>\n<p>Cursul de tratament e simptomatic. Asemenea copii au nevoie de o diet\u0103 s\u0103n\u0103toas\u0103 \u0219i echilibrat\u0103, dezvoltarea m\u0103surilor care ar putea preveni eventualele complica\u021bii.\u00a0De asemenea, sunt recomandabile exerci\u0163iile fizice \u0219i gimnastica curativ\u0103, care are ca scop \u00eembun\u0103t\u0103\u021birea st\u0103rii de s\u0103n\u0103tate a copilului.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Principala caracteristic\u0103 este sl\u0103biciunea muscular\u0103 asociat\u0103 de atrofia mu\u015fchilor. Boala se dezvolt\u0103 \u00een copil\u0103ria timpurie. E cauzat\u0103 de astfel de factori: a modific\u0103rilor \u00een celulele cornului anterior spinal, prin procesul degenerativ cu o progresie clar\u0103; a schimb\u0103rilor de origine secundar\u0103 \u00een celulele nervoase, precum \u0219i \u00een \u021besutul muscular. \u00a0Cauzele Amiotrofia spinal\u0103 Werding-Hoffmann este ereditar\u0103.\u00a0Conform cercet\u0103rilor, [&hellip;]<\/p>\n","protected":false},"author":28,"featured_media":0,"parent":52975,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"inline_featured_image":false,"footnotes":""},"class_list":["post-54283","page","type-page","status-publish"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Amiotrofia spinal\u0103 la copii \u2013 Werdnig-Hoffmann<\/title>\n<meta name=\"description\" content=\"Principala caracteristic\u0103 este sl\u0103biciunea muscular\u0103 asociat\u0103 de atrofia mu\u015fchilor. 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